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目的探讨脊髓血管母细胞瘤的诊断与治疗。方法报告7例脊髓血管母细胞瘤,就其临床特征、神经影像学特点、手术治疗及预后进行回顾性分析。结果脊髓血管母细胞瘤大多表现为边界清晰的实质性占位,增强后明显均匀的强化,病变周围上、下蛛网膜下腔可见迂曲增粗血管流空影,常伴有脊髓空洞或囊性变。本组7例均经显微手术全切,术后症状明显改善5例,2例无明显变化。结论脊髓血管母细胞瘤的诊断及鉴别诊断主要依靠磁共振成像影像学特点,正确的术前诊断有助于手术全切肿瘤,显微手术能做到肿瘤全切,效果良好。
Objective To investigate the diagnosis and treatment of spinal hemangioblastoma. Methods Seven cases of spinal hemangioblastoma were reported, and their clinical features, neuroimaging characteristics, surgical treatment and prognosis were retrospectively analyzed. Results Spinal cord hemangioblastoma mostly showed a clear and substantial border, enhanced significantly enhanced after the lesions around the upper and lower subarachnoid lesions can be seen tortuous thickening of the vascular shadow, often accompanied by syringomyelia or cystic change. The group of 7 patients were microsurgical total resection, postoperative symptoms were significantly improved in 5 cases, 2 cases no significant change. Conclusion The diagnosis and differential diagnosis of spinal hemangioblastoma mainly rely on the characteristics of magnetic resonance imaging. Correct preoperative diagnosis is helpful for the complete resection of the tumor. Microsurgery can achieve complete tumor resection with good effect.