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已往认为,肝细胞癌的组织学类型与预后无关,但近年来,发现肝纤维板层癌(Fibrolamellar Carcinoma of the Liver)作为一种特殊类型的肝细胞癌,其临床表现和病理改变,尤其预后等方面.都与普通型肝细胞癌有所不同.本文主要对肝纤维板层癌的临床、病理以及新进展综述如下:肝纤维板层癌的命名问题Edmondson于1956年曾经描述过1例年仅14岁女性患者,其肝脏病变的组织形态学特征性改变是由嗜酸性瘤细胞和丰富的纤维间质所构成,并且术后生存时间较长,而提出是一种特殊类型的肝细胞癌.20年以后,Peters在1976年对300例肝细胞癌的病理研究中,又发现与之十分相似的4例尸检及1例活
In the past, it was thought that the histological type of hepatocellular carcinoma has nothing to do with the prognosis. However, in recent years, Fibrolamellar Carcinoma of the Liver has been found as a special type of hepatocellular carcinoma. Its clinical manifestations and pathological changes, especially prognosis, etc. All aspects are different from the common type of hepatocellular carcinoma. This article mainly summarizes the clinical, pathological and new developments of hepatic fibrolamellar carcinoma as follows: Naming of hepatic fibrolamellar carcinoma Edmondson described a case of only 14 year old female in 1956. In patients, histopathological changes of liver lesions are composed of eosinophilic cells and abundant fibrous stroma, and the survival time is longer, and it is proposed to be a special type of hepatocellular carcinoma. After 20 years In the pathological study of 300 cases of hepatocellular carcinoma in 1976, Peters found 4 autopsy cases and 1 case that were very similar to it.