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作者报告12例发生在鼻腔鼻窦的恶性纤维组织细胞瘤。本病骨质破坏严重、范围广泛。全部病人进行了X线常规检查,4例病人进行了CT扫描,明确了肿瘤侵及的范围。诊断主要依靠组织病理学,做了电镜观察。治疗以手术加放疗为主。对发生在鼻腔鼻窦恶性纤维组织细胞瘤的临床及病理特点、治疗与预后进行了讨论。
The authors report 12 cases of malignant fibrous histiocytoma in the nasal cavity and sinuses. The disease has severe bone destruction and a wide range of conditions. All patients underwent routine X-ray examinations and 4 patients underwent CT scans to clarify the extent of tumor invasion. The diagnosis mainly relies on histopathology and electron microscopy. Treatment is based on surgery plus radiotherapy. The clinical and pathological features, treatment and prognosis of malignant fibrous histiocytoma of the nasal cavity and sinuses were discussed.