论文部分内容阅读
作者报告1例长期患大疱性表皮松解症(EB)患者的上颌窦和硬腭发生鳞状细胞癌,并描述其CT表现。患者男,37岁,隐性营养障碍性EB伴鼻分泌物和硬腭不愈性溃疡1年。因颈胸段食道狭窄致咽下困难病史20年。巨结肠经常发生粪便嵌塞并行多次手术以缓解痉挛和切除瘢痕,6年前成功地进行了右膝鳞状细胞癌广泛切除及植皮手术。患者有一姊亦患EB于20岁死亡。
The authors report a case of squamous cell carcinoma of the maxillary sinus and hard palate in patients with chronic bullous epidermolysis bullosa (EB) and describe their CT findings. Male patient, 37 years old, with latent dystrophic EB with nasal secretions and hard hemorrhoids ulcer for 1 year. A 20-year history of dysphagia due to cervical esophageal stenosis. The coma involved with fecal impaction and multiple surgical procedures to relieve spasms and resection scars. Successfully performed extensive resection of the right knee squamous cell carcinoma and skin graft surgery 6 years ago. One patient who also had EB died at the age of 20.