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目的 报道移植肾复发性局灶、节段性肾小球硬化 (FSGS)二例。方法 肾病综合征、肾功能衰竭患者 2例 (1 5岁 ,2 5岁 ) ,病理诊断均为FSGS ,分别于肾移植术后 2周和 1年半复发肾病综合征。移植肾病理特征 :肾小球节段性硬化 ,以IgM为主的免疫球蛋白局灶性块状沉积于系膜区 ,弥漫性上皮细胞变性及足突融合 ,诊断FSGS复发。采用血浆置换和血管紧张素转换酶抑制剂(ACEI)治疗。结果 经血浆置换和ACEI治疗后 ,尿蛋白明显减少 ,随访 1 2个月以上 ,无进一步恶化 ,血肌酐稳定。结论 FSGS采用血浆置换及ACEI治疗效果良好
Objective To report two cases of recurrent renal allograft and segmental glomerulosclerosis (FSGS). Methods Nephrotic syndrome, renal failure in 2 patients (15 years old, 25 years old), pathological diagnosis were FSGS, respectively, at 2 weeks and 1 year and a half after renal transplantation recurrent nephrotic syndrome. Graft renal pathological features: segmental glomerular sclerosis, IgM-based immunoglobulin focal mass deposition in the mesangial area, diffuse epithelial degeneration and foot process fusion, diagnosis of FSGS recurrence. Treatment with plasma exchange and angiotensin converting enzyme inhibitor (ACEI). Results After the plasma exchange and ACEI treatment, urinary protein was significantly reduced, followed up more than 12 months without further deterioration, stable serum creatinine. Conclusion FSGS plasma exchange and ACEI treatment effect is good