鼻神经胶质瘤一词系1900年Schmidt首用,较早文献曾用神经节瘤、纤维胶质瘤、神经节膜无成胶质细胞瘤、鼻额脑迷离瘤等。本病少见,至今只有百例报告。多数在初生及幼年发现,个别病例成年后才表现明显。作者报告三个新病例,皆为4—6个月的婴儿,其中一例合并鼻裂(bifid nose)畸形。临床表现鼻外型占60％,鼻内型30％,混合型10％。鼻外型表现为皮下坚实光滑的肿块,似与下面的骨质粘连,表面皮肤发红或发蓝, The term “nose glioma” was first used by Schmidt in 1900. Earlier literature used ganglionoma, glioma, ganglion-ized glioblastoma, and nose-frontal brain tumors. This disease is rare, so far only 100 cases have been reported. Most of them were found in newborns and young children, and individual cases only became apparent after they became adults. The authors reported three new cases, all of which were 4-6 months of age, including one with a bifid nose deformity. The clinical appearance of nasal type accounted for 60%, intranasal 30%, mixed 10%. The appearance of the nasal part is a solid, smooth, lumpy subcutaneous mass that seems to adhere to the underlying bone and the surface of the skin is red or blue.