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恶性组织细胞增生症(malignanthistiocytosis)是单核组织细胞系统的组织细胞及其祖系异常增生,多器官广泛局灶浸润的进行性恶性疾病。本病罕见,发展迅速,预后极差。本文综合报道5例,并结合文献复习分析讨论如下。1临床资料1.1一般资料:恶性组织细胞增生症5例,其中男4例
Malignant cell histiocytosis (malignanthistiocytosis) is a progressive malignancy in which mononuclear histiocyte system tissue cells and their ancestors are abnormally hyperplastically infiltrated by multiple organs. The disease is rare, rapid development, and poor prognosis. This article comprehensively reported 5 cases, and combined with literature review analysis and discussion as follows. 1 Clinical data 1.1 General information: 5 cases of malignant histiocytosis, including 4 males