本文报道２例多巴反应性肌张力不全，表现为儿童起病的最先累及下肢的肌张力不全，伴有帕金森病的症状和体征，对小剂量多巴有持续７年以上的极好反应。并对本病的名称、发病机制、临床表现、诊断和治疗予以探讨 This article reports 2 cases of dopa-responsive hypertonia, manifested as the first onset of children involving the lower limbs dystonia, accompanied by Parkinson’s disease symptoms and signs of small doses of dopa for more than 7 years of excellent reaction. And the name of the disease, pathogenesis, clinical manifestations, diagnosis and treatment to be explored