小儿胆脂瘤较成人胆脂瘤病变极易复发,病情也复杂。通常先天性胆脂瘤与后天性胆脂瘤不易区别,正确掌握病情较为困难。该文对小儿胆脂瘤临床表现、发病部位、听小骨病变、复发与残留、手术方法及效果等作了报道。 先天性胆脂瘤:26例(26耳),男14例,女12例。第1次手术时年龄2～15岁,平均7岁9个月。体检时 Pediatric cholesteatoma more easily than the recurrence of adult patients with cholesteatoma, the condition is complicated. Often congenital cholesteatoma and acquired cholesteatoma is not easy to distinguish the correct grasp of the disease is more difficult. This article reports the clinical manifestations, pathogenesis of pediatric cholesteatoma, small bone lesions, recurrence and residual, surgical methods and effects. Congenital cholesteatoma: 26 cases (26 ears), 14 males and 12 females. The first surgery at the age of 2 to 15 years, an average of 7 years and 9 months. Physical examination