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肺泡蛋白沉着症(pulmonary alveolarprotinosis,PAP),Rosen 于1958年首先报道27例,并认为是少见的疾病。近10余年诊断方法不断进步,各国 PAP 的报道逐渐增多。我国于1965年报道1例,生前误断为结节病,尸检证实为 PAP。1980年又发现4例,2例肺活检、2例尸检证实。足见 PAP 并非少见。PAP 极易与其他肺疾病混淆,造成误诊。本文复习有关文献,着重概述诊断和治疗的进展。临床资料病因 PAP 的病因迄今尚未明确。可能由于吸入物理、化学物质引起的肺脏非特异性反
Alveolar proteinosis (pulmonary alveolarprotinosis, PAP), Rosen first reported in 1958, 27 cases, and is considered a rare disease. Nearly 10 years of diagnostic methods continue to progress, reports of PAP gradually increased. One case was reported in China in 1965, and her life was misdiagnosed as sarcoidosis. The autopsy was confirmed as PAP. In 1980, another 4 cases were found, 2 cases of lung biopsy and 2 cases of autopsy confirmed. PAP is not uncommon. PAP easily confused with other lung diseases, resulting in misdiagnosis. This article reviews the literature, highlighting the progress of diagnosis and treatment. The etiology of PAP causes etiology has not yet clear. May be due to inhalation of physical, chemical lung caused by non-specific anti-