目的　提高对原发性肝肉瘤的诊治水平。方法　回顾性分析原发性肝肉瘤14例的临床资料。结果　14例全部误诊,能手术切除者仅3例。本组病人治疗后平均生存6个月;3例手术切除者术后分别生存4年,6个月,3个月;单纯剖腹探查最长存活4个月,平均15个月。结论　肝肉瘤术前诊断困难,误诊率高,预后差。 Objective To improve the diagnosis and treatment of primary hepatic sarcoma. Methods The clinical data of 14 cases of primary hepatic sarcoma were retrospectively analyzed. Results All the 14 cases were misdiagnosed and only 3 were able to be surgically resected. After treatment, the patients in this group survived for an average of 6 months; 3 patients who underwent surgical resection survived for 4 years, 6 months, and 3 months respectively; and laparotomy only survived for a maximum of 4 months, with an average of 15 months. Conclusions Preoperative diagnosis of liver sarcoma is difficult, with high misdiagnosis rate and poor prognosis.