Sturge-Weber综合征系一特殊的先天性脑血管畸形病,为神经皮肤血管瘤病的一种少见类型,国内报告不多,作者最近见一典型病例,现报告如下。病历摘要郭某,男,16岁,出生时即见颜面左侧有大片红斑,于1～2岁曾因高热,突然四肢抽搐,意识不清,两眼上吊,口吐白沫,历时数分钟缓解又反复发作10余次而住院3次,此后14年未再发病。本次于4 Sturge-Weber syndrome is a special type of congenital cerebrovascular malformations, is a rare type of neuro-cutaneous hemangiomatosis. There are not many domestic reports. The authors recently found a typical case and are reported as follows. Medical history Abstract Kwak, male, 16 years old, see the face of birth at the time there is a large erythema on the left, had a fever in 1 to 2 years old, suddenly convulsions of limbs, unconsciousness, hanging two eyes, foaming at the mouth for several minutes Relieved and recurrent episodes more than 10 times and hospitalized 3 times, 14 years after no recurrence. This time at 4