脑室外神经细胞瘤是2007年WHO中枢神经系统肿瘤分类系统新列出的8种实体之一,属少见神经系统原发性肿瘤[1]。其发病部位为除脑室外的大脑半球、丘脑、小脑及桥脑等,发生于脊髓者十分罕见[2]。现报告1例原发于脊髓的脑室外神经细胞瘤,讨论其特殊发病部位、病理及影像学特点。1临 Extracerebral neuroblastoma is one of the eight newly listed entities in the WHO classification system of the central nervous system in 2007 and is a rare primary tumor of the nervous system [1]. The incidence of parts of the brain in addition to the cerebral hemisphere, the thalamus, cerebellum and pons and so on, occurred in the spinal cord are very rare [2]. Now report a case of primary cerebral neurinoma in the spinal cord to discuss its special pathogenesis, pathology and imaging features. 1 Pro