先天性(遗传性)球型红细胞增多症(SCTS)是红细胞膜先天性缺陷的疾病,先天性溶血性贫血之一,此病极为少见,我院1980年发现一例报告如下: 病例摘要患者女性,10岁,住院号3568,于1980年5月11日因发烧伴面色苍白一周,以贫血待查收住。患者入院前一周,因吃四根冰棒后而发热,面色苍白,全身乏力,曾在家长单位医务室肌注卡那霉素,服退热剂等,约二天退热,但头晕、面色苍白加剧,食欲不振,无出血现象。门诊血化验RBC160万/mm~3,WBC6400/mm~3,BPC10.9万/mm~3, Congenital (hereditary) polycythemia vera (SCTS) is a congenital defect of erythrocyte membrane disease, congenital hemolytic anemia, the disease is extremely rare, our hospital found a case in 1980 as follows: Case Summary Female patients, 10 years old, hospital number 3568, on May 11, 1980 because of fever with pale pale week, awaiting investigation with anemia. One week prior to admission, patients were feverish, pale and malaria after eating four popsicles. They had intramuscular injection of kanamycin and antipyretics in the parent unit’s infirmary. About two days after the fever, they dizzy and pale. , Loss of appetite, no bleeding. Outpatient blood test RBC160 million / mm ~ 3, WBC6400 / mm ~ 3, BPC109 000 / mm ~ 3,