耳硬化症是由于前庭窗部的硬化症病灶使镫骨底板固定,致中耳传导性障碍。硬化灶不在前庭窗,而发生于耳蜗骨壁,引起耳蜗性感音障碍,称内耳硬化症(inner ear otosclerosis)。【提出内耳硬化症的根据】Meurman等(1962)提出在40岁以下的临床性耳硬化症163例中伴有内耳障碍者占24.5%;Carhart(1963)提出在镫骨固定的181例362耳中,在250～4000Hz骨导损失10dB以上者209耳,占57.5%;Schuknecht等(1974)在92耳临床性耳硬化症中,发现62耳为混合性聋,占67.4%。业已证明,耳硬化症病变不常限于前庭窗周围。Nylen(1949)在121例耳硬化症颞骨的病理组织学检查中发现病变在前庭窗者占90%,而引起镫骨固定者仅占50%,其余病变在圆窗者占40%,耳蜗骨壁者35%,内耳道者30%,半规管者15%。据上述事实和有镫骨固定的耳硬化症常伴有内耳功能障碍,推测耳硬化症所伴发的内耳性聋是耳蜗骨壁 Otosclerosis is due to sclerosis of the vestibular window of the sclera plate fixation, causing middle ear conduction disorders. Sclerosis is not in the vestibular window, but occurred in the cochlear wall, causing cochlear hearing loss, called ear inner ear (inner ear otosclerosis). According to Meurman et al. (1962) proposed that 163.5% of patients with clinical otosclerosis under 40 years of age had internal hearing loss, and Carhart (1963) proposed 181 patients with 362 ears , 209 ears (57.5%) suffered bone loss more than 10 dB at 250-4000 Hz. Schuknecht et al. (1974) found that 62 ears were mixed hearing loss, accounting for 67.4% of 92 ears. It has been demonstrated that otosclerosis lesions are not often confined to the vestibular window. Nylen (1949) found that in 121 cases of otosclerosis temporal bone histopathological examination found that the lesions in the anterior chamber window accounted for 90%, while causing stapes fixation only 50%, the remaining lesions in the round window accounted for 40% of the cochlear 35% of the wall, 30% of the ear canal, and 15% of the semiconventional tube. According to the above-mentioned facts and the ear tarsal otitis media is often accompanied by dysfunction of the inner ear, it is speculated that ear deformity associated with ear sclerosis is the cochlear wall