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钟某,男,5岁,广东博罗县人。因双眼睑下垂50余天,左眼球活动障碍20天于1986年8月28日入院。患儿于50天前无明显诱因出现颈部向左倾斜伴强直无力,两天后左眼睑下垂,次日右眼睑亦下垂。近20天来左眼球固定居中,右眼球上下活动增多。患儿足月顺产,平素身体健康,无外伤史。姐弟共四人,大姐六岁起双眼睑下垂,诊断“重症肌无力”,服“新斯的明”后明显减轻,二姐及大哥未见类似表现;其父母非近亲结婚。检查:发育正常,营养良好,神智清楚,欠合作;皮肤巩膜无黄染,浅表淋巴结不肿大,甲
Zhongmou, male, 5 years old, Boluo County, Guangdong Province. More than 50 days due to double eyelid ptosis, left eye movement disorders 20 days in 1986 August 28 admission. Children with no obvious incentive to appear 50 days ago left incline with tetanic weakness, left ptosis two days later, the next day the right eyelid also droop. In the past 20 days, the left eyeball was fixed centrally and the right eyeball was increased. Children with full-term follow-up, usually healthy, no history of trauma. A total of four siblings, elder sister six-year-old double eyelid ptosis, the diagnosis of “myasthenia gravis”, serving “neostigmine” significantly reduced after the second sister and brother no similar performance; their parents marry non-relatives. Check: normal development, good nutrition, clear mind, owed cooperation; skin sclera no yellow dye, superficial lymph nodes are not enlarged, A