Sturge—Weber综合征又称脑—三叉神经血管瘤病,较罕见,报告1例如下: 患者,男,13岁,出生即见左面部有1指头大紫色红斑,近5年来红斑逐渐扩大至左额颞部、眼眶周围、面颊及鼻的左外侧。半岁开始有发作性右上肢抽搐,多年来每月发作1～2次,有时神志丧失,每次发作几分钟至10余分钟。2岁开始学走路,现右上肢肌肉萎缩、力弱,活动不灵活,未上学,智力低下。非近亲结婚,足月顺产,无家族史。 体检:发育尚可,神志清,智力差,简单减数困难。左三叉神经Ⅰ—Ⅱ支分布区及左侧顶枕区大片紫红色血管瘤,左眼眶周围为暗红色,血管瘤累及左侧 Sturge-Weber syndrome, also known as brain-trigeminal neovascular disease, is relatively rare, a report is as follows: The patient, male, 13 years old, was born to see the left facial finger purple big erythema, erythema gradually expanded to the left Frontotemporal, periorbital, cheek and nasal left lateral. Six months old, onset of upper right limb seizures, seizures 1 to 2 times per month over the years, and sometimes loss of consciousness, each attack a few minutes to 10 minutes. 2 years old began to learn to walk, right upper extremity muscle atrophy, weak, activities are not flexible, did not go to school, mental retardation. Non-relatives married, full-term birth, no family history. Physical examination: development is acceptable, clear-minded, poor intelligence, a simple number of difficulties. Left trigeminal nerve Ⅰ-Ⅱ branch distribution and the left top of the occipital parietal large purple hemangioma, left orbital around dark red, hemangioma involving the left