先天性肺动脉缺如,是一种罕见的肺血管畸形,多发生在右侧,而发生在左侧者则更为罕见,现将2例报告如下。例1:男,15岁,因阵发性咳嗽、咳痰、乏力、盗汗5年,加重两月来院就诊。查体:左肺中下野可闻及湿性罗音,营养发育差,体质瘦弱。X线表现:后前位胸片见,右肺门阻影增大浓密,右肺 Congenital absence of pulmonary arteries, is a rare pulmonary vascular deformity, occurred in the right side, while in the left are more rare, now 2 cases are reported as follows. Example 1: Male, 15 years old, due to paroxysmal cough, sputum, fatigue, night sweats 5 years, increased two-month hospital visit. Physical examination: the middle and lower lungs can be heard from the wet rales, poor nutrition, physical weakness. X-ray performance: see the anterior chest radiograph, right hilar enlargement, right lung obstruction