脊索瘤起源于残留脊索组织的恶性肿瘤,约占原发性骨肿瘤的3～4％。50％发生在骶尾部,其余在颅底或椎骨。过去,多采用肿瘤内剜除或沿着肿瘤包膜的边缘切除的手术方法治疗骶尾部脊索瘤。但是,这些方法常因残留肿瘤组织的复发而终致病人死亡。近来有人施行连同肿瘤外一部分正常组织一併切除的根治性手术,效果虽满意,但只适于肿瘤范围较小者。然而,多数骶尾部脊索瘤患者早期症状轻微,常待肿瘤明显增大,出现直肠、泌尿道或神经压迫症状始到医院就诊。增加了治疗上很大困难。1976年Gunterberg等研究指出:单纯保留第一骶骨上半部,骨盆有足够的强度使病人维持站立。保留单侧骶神经或保留一侧上方三条及另一侧上方两条骶神经,可基本保存肛门,直肠和泌尿生殖系统的机能。如果仅保留双侧第一骶神经,则可维持双侧下肢功能,平地步态正常,只上坡困难。但是,会出现大小便失禁,生 Chordoma originates from malignant tumors in the residual spinal cord tissue and accounts for about 3-4% of primary bone tumors. 50% occur in the sacrococcygeal end and the remainder in the skull base or vertebrae. In the past, sacrococcygeal chordomas were treated surgically with tumors excised or trimmed along the margins of the tumor envelope. However, these methods often result in the death of the patient due to the recurrence of residual tumor tissue. Recently, radical surgery with the removal of a portion of the normal tissue outside the tumor has been performed. Although the effect is satisfactory, it is only suitable for those with a small tumor size. However, most patients with sacrococcygeal appendix tumors have mild symptoms at the early stage, and often require a significant increase in the size of the tumor. The symptoms of rectal, urinary tract, or nerve compressions are seen in the hospital. Increased treatment difficulties. Gunterberg et al. (1976) pointed out that the upper part of the first metatarsal is preserved and the pelvis has enough strength to maintain the patient’s standing. Keeping the unilateral sacral nerve or retaining the top three sides and the top two phrenic nerves on the other side can basically preserve the function of the anus, rectum and urogenital system. If only the bilateral first sacral nerve is preserved, bilateral lower extremity function can be maintained, and the gait in the plain is normal, and it is only difficult to uphill. However, there will be incontinence, birth