肺发育不全是一种少见的先天性疾病，临床多见于婴幼儿，成年人少见，伴有其它肺部疾患更为罕见。1991~1999年，我院先后收治2例先天性单肺发育不全伴自发性气胸者，经手术治疗效果良好，现报告如下。1 临床资料例1，男性，47岁，18年前于劳动时突然发生呼吸困难，右侧胸痛，当 Lung hypoplasia is a rare congenital disease, more common in infants and young children clinically, adults rare, accompanied by other lung diseases are more rare. From 1991 to 1999, our hospital has admitted 2 cases of congenital unilateral lung dysplasia with spontaneous pneumothorax, the effect of good surgical treatment, are as follows. 1 clinical data Example 1, male, 47 years old, 18 years ago, sudden dyspnea in labor, right chest pain, when