间质性肺纤维化是一组异型的(heterogeneous)疾病。主要发生于肺间质,亦可累及肺泡上皮细胞、肺毛细血管内皮细胞和肺动静脉。病种约有130之多。其分类尚未统一,或按病理变化,或按X线表现分类。多数学者倾向于将本病分为病因已明和病因未明两类(表1、2)。 Interstitial lung fibrosis is a heterogeneous group of diseases. Mainly occurs in interstitial lungs, but also involving the alveolar epithelial cells, pulmonary capillary endothelial cells and pulmonary artery and vein. About 130 as many diseases. The classification has not been uniform, or according to pathological changes, or by X-ray performance classification. Most scholars tend to be divided into the cause of the disease has been etiologically and etiologically unknown two types (Table 1, 2).