本文报道1例患者，因间断右腰部疼痛1个月余、加重1周入院并行腹腔镜根治性右肾切除术，术后诊断为右肾纤维肉瘤。患者拒绝进一步放化疗，术后第11天出院。术后1年查胸部CT示肝右叶背膜下肿物。于外院行手术治疗，术后诊断为右肾纤维肉瘤肝转移。术后随访4个月未见复发和转移。“,”A patient with intermittent right lumbar pain for more than one month and aggravating for one week was reported. The right laparoscopic radical nephrectomy was performed, and fibrosarcoma of the right kidney was diagnosed. The patient refused further radiotherapy or chemotherapy and was discharged on the 11th after surgery. One year after operation, the patient underwent chest CT, and subdural tumor of right lobe of liver was detected. A surgery was performed in another hospital, and liver metastasis from right renal fibrosarcoma was diagnosed. He was alive four months after operation.