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红细胞生成性脓卟啉病(erythropoietic protoporphyria)并不罕见,但国内报道较少。我院近日收治1例,现报告于下。 患儿 女,9岁。主因颜面与双手背部反复肿痛、化脓、结痂7年半,双足肿痛5天于1996年6月20日入院。患儿自1岁半始,每年3至4次出现面部与双手背部红、肿、痒、痛,剧烈时哭闹。继之出现散仜皮疹,中央化脓,甚至溢脓、结痂,久后形成瘢痕。发作无明显季节差异,日光曝晒可使皮损加重。疼痛重时患儿喜将双手置于凉水中。从无多汗、乏力、吞咽因难、腹痛及尿色异常。数年间辗转于几所城市大医院,分别珍为“日光性皮炎”,“风湿病”,“皮肤过
Erythropoietic protoporphyria is not uncommon, but less reported in China. I hospital recently admitted in 1 case, the report is now under. Children with children, 9 years old. Mainly due to facial and hands repeated back pain, purulent, scab 7 and a half years, bipedal pain 5 days in June 20, 1996 admission. Children from the age of 1 year old, 3 to 4 times a year appear facial and hands back red, swollen, itchy, painful, crying violently. Followed by the emergence of loose skin rashes, purulent, or even overflow pus, scab, a long time to form scars. Seizures no significant seasonal differences, sun exposure can make the skin lesions worse. Children with severe pain when the hi will be placed in cold water. From no sweating, fatigue, difficulty swallowing, abdominal pain and abnormal urine color. A few years was removed in several large hospitals in cities, respectively, Jane as “dermatitis”, “rheumatism”, "skin too